Vol. 45 (5): 1076-1077, September – October, 2019
María Medina-González 1, Jorge Panach-Navarrete 1, Lorena Valls-González 1, Ana Castelló-Porcar 1, Jose María Martínez-Jabaloyas 1
1 Department of Urology. University Clinic Hospital of Valencia, Facultat de Medicina i Odontologia, Universitat de València, Spain
Introduction: OHVIRA syndrome is a rare entity characterized by renal and Mullerian anomalies. The objective of the video is, through a clinical case, to discuss the importance of diagnosis, management and treatment, to avoid the complications that this syndrome entails, and to improve the long-term prognosis.
Materials and Methods: We report the case of a 10-year-old girl who consulted for abdominal pain, being diagnosed with OHVIRA syndrome. We describe the diagnosis and the surgical technique. In addition, we perform a systematic review in PubMed to report the published literature of this topic and we show the optimal management of this pathology.