Laparoscopic nephroureterectomy as treatment in obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome

Vol. 45 (5): 1076-1077, September – October, 2019

doi: 10.1590/S1677-5538.IBJU.2018.0430


VIDEO SECTION


María Medina-González 1, Jorge Panach-Navarrete 1, Lorena Valls-González 1, Ana Castelló-Porcar 1, Jose María Martínez-Jabaloyas 1
1 Department of Urology. University Clinic Hospital of Valencia, Facultat de Medicina i Odontologia, Universitat de València, Spain

ABSTRACT

Introduction: OHVIRA syndrome is a rare entity characterized by renal and Mullerian anomalies. The objective of the video is, through a clinical case, to discuss the importance of diagnosis, management and treatment, to avoid the complications that this syndrome entails, and to improve the long-term prognosis.
Materials and Methods: We report the case of a 10-year-old girl who consulted for abdominal pain, being diagnosed with OHVIRA syndrome. We describe the diagnosis and the surgical technique. In addition, we perform a systematic review in PubMed to report the published literature of this topic and we show the optimal management of this pathology.

ARTICLE INFO

Available at: https://www.intbrazjurol.com.br/video-section/20180430_Medina-Gonzalez_et_al

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